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Abstract
Solitary fibrous tumor (SFT) is a rare mesenchymal neoplasm with fibroblastic differentiation that can occur in different parts of the human body. The majority of SFTs are benign; however, approximately 20 % of these, dedifferentiated SFTs, have an aggressive clinical course. The mainstay treatment for SFTs, as for many other soft tissue tumors, is surgery with microscopic margin-negative (R0) resection. Chemotherapy and radiotherapy are not effective in treating SFT. As SFT usually occurs in young patients and involves nearby organs and structures, patients with SFT should undergo all instrumental diagnostics such as MRI, CT and endoscopy before treatment decisions are made. The volume of surgery should be carefully planned to maximize the preservation of adjacent organs and hence the quality of life of the patient, while strictly adhering to oncological principles.
Case description. We describe a case of successful treatment of a young patient with preservation of quality of life and all physiological functions: defecation, urination, and sexual function. Multiple resection of the bladder with removal of the areas involved in the tumor process, but with preservation of the organ itself (bladder) was performed.
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